Yintoni i-scleroderma

Ihlabathi lomqolo kunye nomzimba wethu ngokubanzi iidilesi zithathela ingqalelo uthotho lweengqwalasela ekufuneka zigcinwe engqondweni, njengokoí indlela yokwazisaón malunga nezifo ezahlukeneyo kunye notshintsho olunokubandezeleka emzimbeni. kwesi sihlandloón siza kugxila ekuthetheni nge i-scleroderma, isifo esingaziwayo ngabantu abaninzi ekufuneka saziwe, ngaphezu kwakho konke ukwaziábangababoíntomas, ngokuxilongwaóstico kunye nonyango oluhambelanayo.

Isalathiso

¿Intonié i-scleroderma?

I i-sclerodermayindlela eyaziwa ngayo inkqubo ye-sclerosisémica, yi isifo se-autoimmune crónica ikakhulu ichaphazela ulusu, kodwa kwakhonaéayinakuchaphazela abanye óamalungu afana namathumbu, hayi riñón, intliziyoón, amathumbu…, ukuba ngomnye wabo 50.000 abantu.

Ngenxa yesi sifo, Abo bantu babandezelekayo bayaqaphela ukuba ulusu lwabo luba lukhuni njani kwaye rílukhuni ngenxa yokuqokelelana ngokugqithisileyoón yeentambo zentamoágeno. Okufanayo kuyenzeka ngokuqinisekileyo óamalungu, nto leyo enokwenza kube nzima kubo ukusebenza, nento oyithethayo.

Esi sifo sithathwa njengenkquboémica kuba inokuchaphazela ezahlukeneyo óamalungu, kodwa ayizizo zonke izigulana ezibonwa nge óamalungu angaphakathi achaphazelekayo, kwaye kwezinye iimeko úEyona nto ichaphazelekayo lulusu., iimeko apho ubunzima besifo buncinci.

Iimbangela ze-scleroderma

Ngokuphathelele oonobangela bembonakaloóhayi kwesi sifo, Kufuneka sihlale siyikhumbula loo nto oonobangela bayo abaziwa, kwaye inokuvela nakweyiphi na iminyaka. Nangona kunjalo, sí Yintoni máKuyinto eqhelekileyo ukubonakala kwabasetyhini abaneminyaka ephakathi. Ukwengeza, izehlo zayo ziyaziwa ngokunyuka kumaqela abantu abavezwe kwiimveliso ezithile tóamakhwenkwe, nangona ubukhulu becalaíamaxesha amaninzi yenzeka ngesizathu esingaziwayo.

Njengoko ayisosulelo okanye isifo sofuzo, amalungu osapho okanye abantu abaphethwe ngabo i-scleroderma akufunekanga ithotyelwe phantsi kwayo nayiphi naún iimviwo ningúakukho didi lovavanyo.

Izilonda eziveliswa yi-scleroderma

Inkalo ehlala ikhathaza abo bagula sisifo, kukwazi uhlobo lomonzakalo olunokubangelwa sisifo, kule meko, ukusuka i-scleroderma, isifo ivelisa izilonda zolusu kwaye kananjaloén inokubenza kwezinye óamalungu angaphakathi.

Ekuqaleni, ezi zilonda zivela ngendlela yokuvuvukala.ón, ethi kamva iguquke ibe lukhuni, ngenxa yokuqokelelaóOkugqithisiweyo n of a kakhulu r imicuíikhaphetshu gidaságeno, ukufumana ulusu ukufumana ukuhambelana kwefibrous.

Xa ezi nzakala zichaphazela abanye óamalungu, njengemiphunga okanye umgudu wokwetyisa, nazo ezién iba ríiqinile kwaye inentambo, yintoni eyenza bangasebenzi kakuhle, nengxaki ebandakanya oku.

I-systemic sclerosisémica además ithintela umngcipheko wegaziíneo, kuba ivelisa i-occlusionón kwabancinciñImithambo kunye neecapillaries ezithwala igazi kwizicubu kwaye zinokuvelisa i-síiimpawu kunye nezilonda ezifanayo nezo zezinye izifo zokujikeleza kwegazi, Intoni úizilonda kunye neentlungu kwiminwe.  Kukho ezinye izigulana enokuthi yenzeke into efanayo kwezinye óamalungu.

Síiimpawu ze-scleroderma

Emva kokuba ukwenzakala kwakho kwaziwa, kufuneka uyazién kunyeángabo síiimpawu eziveliswa yi i-scleroderma inkqubo ye-sclerosisémica, edla ngokuqala ngokudumba kancinaneónolusu lwezandla neenyawo, ngamanye amaxesha kakhuluéakukho buso, makwandisweéukusasazeka ngamalungu kwaye oko kunokuchaphazela umzimba wonke.

Emva koko ulusu lunokuba ríiqinile kwaye inzima, umhambi ngezonquloéukwenza kube nzima ukuyicinezela kwaye ngamanye amaxesha kubangela ukuba ukunyakaza kwamalungu kuthintelwe. Kukwaqhelekile ukuba kubekho utshintsho lombala.óHayi yezandla leyo, xa ibhengezwe kufrío, baba ngokugqithisileyo pálidas kunye nodlwengulo kamvaáiiceos, njengoko isifo siqhubela phambili, ihamba kunyeñáukuziva ngamaxesha entlungu okanye ukubetha.

Ezi síiimpawu zaziwa ngokuba fenóngaphantsi kukaRaynaud, nayo leyoén inokunxulunyaniswa nezinye izifo ezininzi okanye ibonakale nakubantu abatshaóuyabona ukuba basempilweni. Kubantu abazisa kuphela le síumpostile, ingcali inakoá ukwenza ezinye iimvavanyo ukuqinisekisa okanye ukukhuphela ngaphandle ukuba i systemic sclerosisémica okanye esinye isifo.

inkqubo ye-sclerosisémica ispaghettién kunokubangela ukudinwa, intlungu edibeneyo, iingxaki zokwetyisa, ukubañukukhankanya, urhudo okanye ubunzima bokuginya, njengokoí ezifana neengxaki ze-cardiorespiratory ezifana nobunzima bokuphefumla, uxinzelelo lwegazióakukho ntlungu yesifuba. Nangona kunjalo, Kufuneka kukhunjulwe ukuba banokubonakalisa iingxaki ezinzulu ze-systemic sclerosis.émica.

Umlinganiseloói-scleroderma stico

Ukuxilongwaói-stico ye i-scleroderma Iphantse isoloko isenziwaés yolwamkelo méugqirha okhethekileyo kwi-rheumatismóuphawu, ukuba udibanise ntoniá ibali lesíiimpawu kunye neskenión Uvavanyo ngokubanzi kunye nolusu.

Ukwengeza, kufuneka kuthathelwe ingqalelo ukuba exáiimenyu ezihambelanayo njengeái-lysis kunye ne-x-reyiíkwi tóirax, kwaye kwezinye iimeko ezithile, ezinye iimvavanyo zokwetyisa okanye i-cardiorespiratory. Ngolu mvavanyo kunokwenzeka ukuphumeza ukuhlelwa okuphezuluón uhlobo lwesifo kwaye uvavanye njengokoí ubungqongqo kunye nobungakanani bayoón ukuya ezahlukeneyo óamalungu, nangona bengeyomfuneko ngokupheleleyo ukuba bakwazi ukuxilonga ukuba isigulane siphethwe i-scleroderma.

Unyango lweScleroderma

Ngokuphathelele unyango lwe i-scleroderma, akukho fáamayeza okanye ezinye iindlela zonyango ezivelisa unyangoón ye-systolic sclerosisémica. Nangona kunjalo, ezininzi zeengxaki kunye nokubonakaliswa okubangelwayo kunokunyangwa ngokufanelekileyo, ngoko zombini pronóImile kangangoko umxhuzulane unokuba nakoá ziyahluka ngokuphawulekayo kuxhomekekeónokuba unyango lwangethuba lufunyenwe okanye hayi.

Kule meko, unokubhenela ekusebenziseni iikhrimu ezahlukeneyo okanye izinto ezikhuselayo.ón, njengokoí njengokukhetha uqheliselo lwentshukumo lweendawo ezichaphazelekayo kunye nokusetyenziswa kwefáamachiza asetyenziselwa ukunweba imithambo yegaziíneos.

kumsebenzión uhlobo lwesifo kunye ne óamalungu achaphazelekayo, isifo sinokucotha kwaye sivelise kuphela ulusu más ihlala kuyo yonke iminyakaños, okanye ngokuqinisekileyo kakhulu ráisicelo kwaye oko kubangela iingxaki ezinzulu kulo mbuzoón kwiiveki.